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Surgical treatment of Hirschsprung’s disease at the National Children’s .. Enfermedad de Hirschprung. Fantobal-Rojas A. Constipación crónica en el niño. La enfermedad de Hirschsprung es un trastorno congénito infrecuente (afecta aproximadamente a 1 de cada recién nacidos en EE. UU.) que provoca. El estreñimiento se debe diferenciar de la enfermedad de Hirschsprung y de alteraciones anatómicas y metabólicas. La evaluación clínica incluye una historia.

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Laparoscopic-assisted approaches for the definitive surgery for Hirschsprung’s disease. Log in Sign up.

The condition typically presents in term neonates with failure to pass meconium in the first days after birth, although later presentation is also common. This study outlines the referral patterns to one centre in the Caribbean The Queen Elizabeth Hospital, Barbados which offers patients definitive surgery for HD and reports on their long term outcome. Authors must state that they reviewed, validated and approved the manuscript’s publication.

Enfermedad de Hirschsprung | Neurology Associates of Kansas

Check for errors and try again. Single-stage transanal endorectal pull-through for Hirschsprung’s disease: Our institution hirscjsprung one experience of having had a patient as outlined above who had a total colectomy and Soave pull-through procedure for presumed total colonic HD based on frozen section analysis which was later not substantiated on paraffin section.

The frequency of HD at young edges is higher on men, but as the edge grows, it occurs more in hiirschsprung. Gastrointestinal function after surgical correction of Hirschsprung’s Disease: In the pediatric population a constipation history since the first month of life, the delay on the elimination of meconium beyond the 24 hours, abdominal distension is a suspicion of Congenital Megacolon.

Case 4 Case 4. Hirschsprung disease is characterised by aganglionosis absence of ganglion cells in the distal colon and rectum.

  LEY 227-06 PDF

Hence it is claimed that the single-stage repair is ideal for use in developing countries where access to medical care may be hampered by poor transportation and communication systems 8.

Enfermedad de Hirschsprung

Data from patients notes were collected to establish demographics, including age at referral and definitive surgery, gender, presenting symptoms, surgical intervention s and definitive procedure.

Synonyms or Alternate Spellings: During the review of patients’ records in this study, it was clear that a number of children who initially hirschsprujg in the neonatal period and re-presented later in childhood were being treated jios necrotizing enterocolitis NEC in the neonatal period when most likely they were experiencing Hirschsprung’s enterocolitis.

Long-term outcome after Hirschsprung’s disease: Hirschsprung disease in the newborn. Edit article Share article Hircshsprung revision history. The child requiring use of both laxatives and enemas was the only one in the series with regular periods of absenteeism from school. The Congenital Megacolon presents agonglionosis in different lengths of the intestine; many times associated to other congenital anomalies.

Bruce et hirschs;rung 16 have reported on their preliminary experience with the use of the rectal suction biopsy some 10 years ago and have recommended its use in the Caribbean setting.

Ineluding sixty-seven consecutive Endorectal Pullthrough procedures. Children referred from the surrounding Caribbean islands were referred at an older age, but their overall outcome was not worse than local Barbadian patients.

Loading Stack – 0 images remaining. Support Radiopaedia and see fewer ads. To assess the surgical outcome of patients with Hirschsprung’s disease HD who were treated in Barbados, establish referral patterns and identify factors which can lead to better management. Medicina de Caldas, vol.

Yanchar NL, Soucy P. Veinte eran varones y siete hembras.

Long term outcome was assessed by the use of a simple questionnaire completed by the junior author MVV after personal or telephone contact with patients, their parents or guardians or the referring hirsschsprung. Megaeystis Illicrocolonintestinal hypoperistalsis synorollle: The most important exam to diagnose this disease is the rectal biopsy of the ennfermedad stenotic segment, which shows the absence of ganglion cells, nerve hypertrophy presence and incresement of the activity of acetycholinesterase.


Over a year period, between July and June27 children were identified with Hirschsprung’s disease HDincluding twenty males and seven females – [male: Hence, functional obstruction develops as a result of a spasm in the denervated colon. In conclusion, Hirschsprung’s disease is a rare cause of constipation and can be successfully managed in Barbados with long-term results comparable to that seen both regionally 18 and internationally 4, 19, 20 despite the availability of limited resources and specialists personnel.

Rectal suction biopsy in the diagnosis of Hirschsprung’s disease: Hence NEC in the term infant should raise one’s suspicion and a rectal suction biopsy performed to exclude HD Surgical treatment is by removal of the affected portion of the colon. In reality, however, many of these factors continue to be lacking in the majority of the Caribbean isles resulting in late diagnosis and referral of children with HD.

[Hirschsprung’s disease: the immunohistochemistry as ancillary method for the diagnosis.]

It can be anatomically divided into four types according to the length of the aganglionic segment:. A new variant of colonic ganglion cell disorders. In protracted cases, marked dilatation can develop, which may progress to enterocolitis and perforation. Special reference to histochemical determination of the acetylcholinesterase activity. Prediction of the outcome of pull-through surgery for Hirschsprung’s disease using acetylcholinesterase activity.